Manufactured by:BT LAB
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ECHA Rabbit Polyclonal Antibody

ECHA Rabbit Polyclonal Antibody

SKU:
ABM179644
Manufacturer SKU
BT-AP09422
Product type
Primary Antibodies
TargetHADHA
ApplicationsWB
Species / reactivityHuman, Mouse, Rat

Manufacturer provenance

Manufactured by:
BT LAB
Sold by:
ABMIUM
Fulfilled from:
Manufacturer facility or confirmed fulfilment location

Know who made it. See the evidence. Buy through one marketplace.

Product description

Background

This gene encodes the alpha subunit of the mitochondrial trifunctional protein| which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits| with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.

Key facts & specifications
Research areas
Cancer, Cardiovascular, Metabolism, Signal Transduction, Tags & Cell Markers
Also known as
ECHA; Trifunctional enzyme subunit alpha; mitochondrial; 78 kDa gastrin-binding protein; TP-alpha) [Includes: Long-chain enoyl-CoA hydratase; EC 4.2.1.17; Long chain 3-hydroxyacyl-CoA dehydrogenase; EC 1.1.1.211;
Host species
Rabbit
Clonality
Polyclonal
Isotype
IgG
Dilution range
WB: 1: 500 - 1: 2000
Immunogen
Synthesized peptide derived from human ECHA
Concentration
1 mg/ml
Purification
The antibody was affinity-purified from rabbit serum by affinity-chromatography using specific immunogen.
Quantity per pack
20ul, 50ul, 100ul
Validation & performance evidence
ABMIUM Validated™ ABMIUM Verified™ Expected performance Not suitable

Application validation matrix

Evidence status by application and model.

EvidenceWB
Applications
Identifiers & database references
Manufacturer SKU
BT-AP09422
Gene ID
3030
UniProt accession
P40939
Storage, stability & shipping
Shelf life
-20°C for 1 year
Storage conditions
-20°C for 1 year
Storage buffer
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.301% sodium azide.
Compliance & documents
Datasheet
Open datasheet
Product manual
Open manual
Frequently asked questions
Who manufactured this product?

This product is manufactured by BT LAB and sold through ABMIUM without relabelling.

Can ABMIUM ship this product internationally?

ABMIUM supports global orders. Availability, shipping requirements and applicable import arrangements are confirmed before fulfilment where required.

Can I check suitability before ordering?

Yes. Send your target, sample, application and experimental conditions through ABMIUM MATCH or technical support.

Is this product for clinical use?

Unless the listing expressly states otherwise, ABMIUM products are supplied for research use only and are not for diagnostic or therapeutic use.

BT LAB
£81.00£69.00